| Inclusion | |
|---|---|
| ≥18 years of age | Diagnosis of ILD |
| Live in the U.S.A. | Progression of ILD within the past two years |
| Forced vital capacity 40-80% | Forced vital capacity 40-80% |
| Diagnosis of myositis or having a myositis autoantibody | Stable standard of care immunosuppression |
| Exclusion | |
|---|---|
| Forced vital capacity less than 40% | Pulmonary hypertension requiring treatment |
| Diffusion capacity greater than 30% | Bleeding or thrombotic risk |
| Listed or actively going through evaluation for lung transplantation | Moderate to severe active myositis |
| Oxygen requirements of >10L at rest | Ongoing serious active, chronic, or recurrent infection |